Retinal vasoproliferative tumor (VPT) describes a vascular nodular tumor arising in the neurosensory retina with associated telangiectasia, lipid exudation, and subretinal fluid. These tumors may occur sporadically (80%) or secondary to other intraocular pathology, such as uveitis, retinitis pigmentosa, toxoplasmosis, toxocariasis, vitreoretinal surgery, familial exudative vitreoretinopathy, Sickle cell disease, retinopathy of prematurity, Coat's disease, Waardenburg's syndrome, and neurofibromatosis type 1.


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