Structure and Morphology of Radial Retinal Folds with Familial Exudative Vitreoretinopathy

Radial retinal folds (RFs) extend from the optic disc to the peripheral retina and generally develop in utero or during the neonatal period owing to severe contractive traction caused by fibrovascular tissues in the periphery.1,2 Although RFs resemble the stalk of persistent fetal vasculature, these disorders are considered to differ. Several diseases have been reported to cause RFs, including familial exudative vitreoretinopathy (FEVR), retinopathy of prematurity, Bloch–Sulzberger syndrome, Norrie disease, and congenital toxoplasmosis.